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Maple Syrup Urine Disease (MSUD)

A rare inherited disorder of branched-chain amino acid (leucine, isoleucine, valine) metabolism. Leads to their accumulation and toxic effects on the brain. Requires a lifelong diet restricting these amino acids. It is a strict contraindication for supplements containing leucine, isoleucine, valine (e.g., BCAAs).

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What to avoid
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What to avoid (8)

  • Adequate Protein Intake Habits Very highTheoretical

    Individuals with Maple Syrup Urine Disease (MSUD), a rare genetic metabolic disorder, cannot process branched-chain amino acids (leucine, isoleucine, valine). Protein intake must be severely restricted and medically supervised to prevent severe neurological damage.

  • BCAA Supplements Very highTheoretical

    If you have Maple Syrup Urine Disease (MSUD), a rare genetic condition, you must strictly avoid BCAAs as your body cannot properly break them down, which can lead to severe health issues.

  • Collagen Peptides Supplements Very highTheoretical

    Individuals with Maple Syrup Urine Disease (MSUD), a metabolic disorder affecting amino acid breakdown, should avoid collagen as it contains branched-chain amino acids (BCAAs) that can be toxic.

  • EAA (Essential Amino Acids) Supplements Very highTheoretical

    Strictly avoid if you have Maple Syrup Urine Disease (MSUD), a genetic disorder that prevents your body from properly breaking down branched-chain amino acids found in this supplement.

  • Naturopathy Practices Very highTheoretical

    Supplements containing branched-chain amino acids (BCAAs: leucine, isoleucine, valine) are strictly contraindicated due to their toxic accumulation in this genetic disorder.

  • Protein Supplements Very highTheoretical

    If you have Maple Syrup Urine Disease (MSUD), a rare genetic condition, all protein supplements must be strictly avoided because of their branched-chain amino acid content.

  • Trypsin Supplements Very highTheoretical

    If you have Maple Syrup Urine Disease (MSUD), avoid oral trypsin as it breaks down proteins into amino acids, including those that are toxic in this condition.

  • Ketogenic Diet Practices LowClinical

    The ketogenic diet is strictly contraindicated for individuals with Maple Syrup Urine Disease, a rare metabolic disorder, as it can worsen their condition.